Vol.108 Issue 12
副腎不全における組織内でのグルココルチコイド代謝:デュアル リリース ヒドロコルチゾン製剤療法の前向き研究
Tissue Glucocorticoid Metabolism in Adrenal Insufficiency: A Prospective Study of Dual-release Hydrocortisone Therapy
Rosemary A Dineen, Julie Martin-Grace, Khalid Mohamed Saeed Ahmed, Angela E Taylor, Fozia Shaheen, Lina Schiffer, Lorna C Gilligan, Gareth G Lavery, Isolda Frizelle, Anjuli Gunness, Aoife Garrahy, Anne Marie Hannon, Paal Methlie, Sverre Husebye Eystein, Paul M Stewart, Jeremy W Tomlinson, James M Hawley, Brian G Keevil, Michael W O’Reilly, Diarmuid Smith, John McDermott, Marie-Louise Healy, Amar Agha, Agnieszka Pazderska, James Gibney, Lucy-Ann Behan, Chris J Thompson, Wiebke Arlt, Mark Sherlock
Vol.108 Issue 12
先天性甲状腺機能低下症における神経発達及び成長の評価:408例を対象とする6年間の追跡調査研究
Assessment of Neurodevelopment and Growth in Congenital Hypothyroidism: Serial 6-Year Follow-up Study of 408 Patients
Eun Kyo Ha, Ju Hee Kim, Hye Ryeong Cha, Gi Chun Lee, Jeewon Shin, Eun Lee, Won Seok Lee, Eun-Gyong Yoo, Mo Kyung Jung, Man Yong Han
Vol.108 Issue 12
MPOWERED試験の非盲検継続試験:先端巨大症におけるオクトレオチド経口カプセル錠の長期有効性及び安全性データ
MPOWERED Trial Open-Label Extension: Long-term Efficacy and Safety Data for Oral Octreotide Capsules in Acromegaly
Maria Fleseriu, Mark Molitch, Alexander Dreval, Yulia Pokramovich, Irina Bondar, Yury Poteshkin, Djuro Macut, Barbara Obermayer-Pietsch, Yossi Gilgun-Sherki, Asi Haviv, Nienke Biermasz, Christian J Strasburger
Vol.108 Issue 12
糖尿病網膜症の重症度と自由行動下モニタリングでの高い血圧及び血清中レニン低値との関連
Associations of Diabetic Retinopathy Severity With High Ambulatory Blood Pressure and Suppressed Serum Renin Levels
Kentaro Sada, Yuichi Yoshida, Kanako Shibuta, Kenichi Kimoto, Shotaro Miyamoto, Yoshinori Ozeki, Mitsuhiro Okamoto, Koro Gotoh, Takayuki Masaki, Katsuhiko Yokoyama, Toshiaki Kubota, Hirotaka Shibata
Vol.108 Issue 12
妊娠中のブドウ糖負荷試験は将来の糖尿病リスクの予測因子である
The Glucose Challenge Test in Pregnancy Identifies Future Risk of Diabetes
Ravi Retnakaran, Baiju R Shah
Vol.108 Issue 12
多発性内分泌腫瘍症1型(MEN-1)に伴う十二指腸・ 膵神経内分泌腫瘍の進行と関連する血中プロテオームシグネチャー
Blood-based Proteomic Signatures Associated With MEN1-related Duodenopancreatic Neuroendocrine Tumor Progression
Johannes F Fahrmann, Amanda R Wasylishen, Carolina R C Pieterman, Ehsan Irajizad, Jody Vykoukal, Ranran Wu, Jennifer B Dennison, Christine B Peterson, Hua Zhao, Kim-Anh Do, Daniel M Halperin, Sunita K Agarwal, Jenny E Blau, Smita Jha, Jaydira Del Rivero, Naris Nilubol, Mary F Walter, James M Welch, Lee S Weinstein, Menno R Vriens, Rachel S van Leeuwaarde, Mark J C van Treijen, Gerlof D Valk, Nancy D Perrier, Samir M Hanash, Hiroyuki Katayama
Vol.108 Issue 12
副腎皮質刺激ホルモン産生腺腫を有する患者における術後の血清コルチゾールとクッシング病の再発
Postoperative Serum Cortisol and Cushing Disease Recurrence in Patients With Corticotroph Adenomas
Michael P Catalino, Dominic T Moore, Natasha Ironside, Alexander R Munoz, Justin Coley, Rachel Jonas, Kathryn Kearns, Le Min, Mary Lee Vance, John A Jane, Jr, Edward R Laws, Jr
Vol.108 Issue 12
1型糖尿病のスクリーニングおよび予防:現在の状況
Screening and Prevention of Type 1 Diabetes: Where Are We?
Kimber M Simmons, Emily K Sims
Vol.108 Issue 12
新たな生存予測因子となりうる年齢および性別調整後のFT3値
Age and Gender Adjusted FT3 Levels as Novel Predictors of Survival
David Strich, Ariel Israel, Shalom Edri, David Gillis
Vol.108 Issue 12
プラダー・ウィリ症候群における悪性腫瘍:大規模国際コホートおよび文献レビューの結果
Malignancies in Prader-Willi Syndrome: Results From a Large International Cohort and Literature Review
Karlijn Pellikaan, Naomi Q C Nguyen, Anna G W Rosenberg, Muriel Coupaye, Anthony P Goldstone, Charlotte Høybye, Tania Markovic, Graziano Grugni, Antonino Crinò, Assumpta Caixàs, Christine Poitou, Raquel Corripio, Rosa M Nieuwenhuize, Aart J van der Lely, Laura C G de Graaff
Vol.108 Issue 11
原発性副甲状腺機能亢進症手術後の長期再発率
Long-term Recurrence Rates After Surgery in Primary Hyperparathyroidism
Muizz Zaman, Laxshika Raveendran, Ayla Senay, Harlan Sayles, Runa Acharya, Mashaal Dhir
Vol.108 Issue 11
先天性副腎過形成(CAH)患者において新生児スクリーニングが成人身長に及ぼす影響
Impact of Newborn Screening on Adult Height in Patients With Congenital Adrenal Hyperplasia (CAH)
Heike Hoyer-Kuhn, Alexander J Eckert, Gerhard Binder, Walter Bonfig, Angelika Dübbers, Stefan Riedl, Joachim Woelfle, Helmuth G Dörr, Reinhard W Holl
Vol.108 Issue 11
副腎不全の早期発見:副腎皮質ジストロフィーの新生児スクリーニングがもたらす効果
Early Detection of Adrenal Insufficiency: The Impact of Newborn Screening for Adrenoleukodystrophy
Jonanlis Ramirez Alcantara, Natalie R Grant, Swathi Sethuram, Amanda Nagy, Catherine Becker, Inderneel Sahai, Takara Stanley, Alyssa Halper, Florian S Eichler
Vol.108 Issue 11
肥満及び非肥満妊娠糖尿病患者における代謝プロファイル
Metabolomic Profiles of Nonobese and Obese Women With Gestational Diabetes
Heidi Sormunen-Harju, Emilia Huvinen, Polina V Girchenko, Eero Kajantie, Pia M Villa, Esa K Hämäläinen, Marius Lahti-Pulkkinen, Hannele Laivuori, Katri Räikkönen, Saila B Koivusalo
Vol.108 Issue 11
CRF1受容体拮抗薬crinecerfontは思春期の先天性副腎過形成患者において副腎アンドロゲン値を低下させる
Crinecerfont, a CRF1 Receptor Antagonist, Lowers Adrenal Androgens in Adolescents With Congenital Adrenal Hyperplasia
Ron S Newfield, Kyriakie Sarafoglou, Patricia Y Fechner, Natalie J Nokoff, Richard J Auchus, Maria G Vogiatzi, George S Jeha, Nagdeep Giri, Eiry Roberts, Julia Sturgeon, Jean L Chan, Robert H Farber
Vol.108 Issue 11
骨折の生涯リスクの遺伝的予測
Genetic Prediction of Lifetime Risk of Fracture
Thao P Ho-Le, Thach S Tran, Huy G Nguyen, Jacqueline R Center, John A Eisman, Tuan V Nguyen
Vol.108 Issue 11
糖尿病患者におけるカナグリフロジンと代謝異常関連脂肪性肝疾患:CANVAS試験からの新たな知見
Canagliflozin and Metabolic Associated Fatty Liver Disease in Patients With Diabetes Mellitus: New Insights From CANVAS
Angel N Borisov, Alexander Kutz, Emanuel R Christ, Markus H Heim, Fahim Ebrahimi
Vol.108 Issue 11
小児X染色体連鎖性低リン血症におけるブロスマブとリン酸塩/活性型ビタミンDとの比較:用量レベル別のサブグループ解析
Burosumab vs Phosphate/Active Vitamin D in Pediatric X-Linked Hypophosphatemia: A Subgroup Analysis by Dose Level
Erik A Imel, Francis H Glorieux, Michael P Whyte, Anthony A Portale, Craig F Munns, Ola Nilsson, Jill H Simmons, Raja Padidela, Noriyuki Namba, Hae Il Cheong, Pisit Pitukcheewanont, Etienne Sochett, Wolfgang Högler, Koji Muroya, Hiroyuki Tanaka, Gary S Gottesman, Andrew Biggin, Farzana Perwad, Angel Chen, Mary Scott Roberts, Leanne M Ward
Vol.108 Issue 11
ベセスダ分類IIIまたはVIの甲状腺結節50,734例を対象としたThyroSeq v3による分子プロファイリング:個別化医療に向けての意義
Molecular Profiling of 50 734 Bethesda III-VI Thyroid Nodules by ThyroSeq v3: Implications for Personalized Management
Simion Chiosea, Steven P Hodak, Linwah Yip, Devaprabu Abraham, Chelsey Baldwin, Zubair Baloch, Seza A Gulec, Zeina C Hannoush, Bryan R Haugen, Lija Joseph, Atil Y Kargi, Elham Khanafshar, Masha J Livhits, Bryan McIver, Kepal Patel, Snehal G Patel, Gregory W Randolph, Ashok R Shaha, Jyotirmay Sharma, Nikolaos Stathatos, Annemieke van Zante, Sally E Carty, Yuri E Nikiforov, Marina N Nikiforova