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JCEM

世界トップレベルの内分泌臨床研究と最先端のClinical Practice Reviewに関する査読誌です。

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Vol.108 Issue 12

副腎不全における組織内でのグルココルチコイド代謝:デュアル リリース ヒドロコルチゾン製剤療法の前向き研究

Tissue Glucocorticoid Metabolism in Adrenal Insufficiency: A Prospective Study of Dual-release Hydrocortisone Therapy

Rosemary A Dineen, Julie Martin-Grace, Khalid Mohamed Saeed Ahmed, Angela E Taylor, Fozia Shaheen, Lina Schiffer, Lorna C Gilligan, Gareth G Lavery, Isolda Frizelle, Anjuli Gunness, Aoife Garrahy, Anne Marie Hannon, Paal Methlie, Sverre Husebye Eystein, Paul M Stewart, Jeremy W Tomlinson, James M Hawley, Brian G Keevil, Michael W O’Reilly, Diarmuid Smith, John McDermott, Marie-Louise Healy, Amar Agha, Agnieszka Pazderska, James Gibney, Lucy-Ann Behan, Chris J Thompson, Wiebke Arlt, Mark Sherlock

Vol.108 Issue 12

先天性甲状腺機能低下症における神経発達及び成長の評価:408例を対象とする6年間の追跡調査研究

Assessment of Neurodevelopment and Growth in Congenital Hypothyroidism: Serial 6-Year Follow-up Study of 408 Patients

Eun Kyo Ha, Ju Hee Kim, Hye Ryeong Cha, Gi Chun Lee, Jeewon Shin, Eun Lee, Won Seok Lee, Eun-Gyong Yoo, Mo Kyung Jung, Man Yong Han

Vol.108 Issue 12

MPOWERED試験の非盲検継続試験:先端巨大症におけるオクトレオチド経口カプセル錠の長期有効性及び安全性データ

MPOWERED Trial Open-Label Extension: Long-term Efficacy and Safety Data for Oral Octreotide Capsules in Acromegaly

Maria Fleseriu, Mark Molitch, Alexander Dreval, Yulia Pokramovich, Irina Bondar, Yury Poteshkin, Djuro Macut, Barbara Obermayer-Pietsch, Yossi Gilgun-Sherki, Asi Haviv, Nienke Biermasz, Christian J Strasburger

Vol.108 Issue 12

糖尿病網膜症の重症度と自由行動下モニタリングでの高い血圧及び血清中レニン低値との関連

Associations of Diabetic Retinopathy Severity With High Ambulatory Blood Pressure and Suppressed Serum Renin Levels

Kentaro Sada, Yuichi Yoshida, Kanako Shibuta, Kenichi Kimoto, Shotaro Miyamoto, Yoshinori Ozeki, Mitsuhiro Okamoto, Koro Gotoh, Takayuki Masaki, Katsuhiko Yokoyama, Toshiaki Kubota, Hirotaka Shibata

Vol.108 Issue 12

妊娠中のブドウ糖負荷試験は将来の糖尿病リスクの予測因子である

The Glucose Challenge Test in Pregnancy Identifies Future Risk of Diabetes

Ravi Retnakaran, Baiju R Shah

Vol.108 Issue 12

多発性内分泌腫瘍症1型(MEN-1)に伴う十二指腸・ 膵神経内分泌腫瘍の進行と関連する血中プロテオームシグネチャー

Blood-based Proteomic Signatures Associated With MEN1-related Duodenopancreatic Neuroendocrine Tumor Progression

Johannes F Fahrmann, Amanda R Wasylishen, Carolina R C Pieterman, Ehsan Irajizad, Jody Vykoukal, Ranran Wu, Jennifer B Dennison, Christine B Peterson, Hua Zhao, Kim-Anh Do, Daniel M Halperin, Sunita K Agarwal, Jenny E Blau, Smita Jha, Jaydira Del Rivero, Naris Nilubol, Mary F Walter, James M Welch, Lee S Weinstein, Menno R Vriens, Rachel S van Leeuwaarde, Mark J C van Treijen, Gerlof D Valk, Nancy D Perrier, Samir M Hanash, Hiroyuki Katayama

Vol.108 Issue 12

副腎皮質刺激ホルモン産生腺腫を有する患者における術後の血清コルチゾールとクッシング病の再発

Postoperative Serum Cortisol and Cushing Disease Recurrence in Patients With Corticotroph Adenomas

Michael P Catalino, Dominic T Moore, Natasha Ironside, Alexander R Munoz, Justin Coley, Rachel Jonas, Kathryn Kearns, Le Min, Mary Lee Vance, John A Jane, Jr, Edward R Laws, Jr

Vol.108 Issue 12

1型糖尿病のスクリーニングおよび予防:現在の状況

Screening and Prevention of Type 1 Diabetes: Where Are We?

Kimber M Simmons, Emily K Sims

Vol.108 Issue 12

新たな生存予測因子となりうる年齢および性別調整後のFT3値

Age and Gender Adjusted FT3 Levels as Novel Predictors of Survival

David Strich, Ariel Israel, Shalom Edri, David Gillis

Vol.108 Issue 12

プラダー・ウィリ症候群における悪性腫瘍:大規模国際コホートおよび文献レビューの結果

Malignancies in Prader-Willi Syndrome: Results From a Large International Cohort and Literature Review

Karlijn Pellikaan, Naomi Q C Nguyen, Anna G W Rosenberg, Muriel Coupaye, Anthony P Goldstone, Charlotte Høybye, Tania Markovic, Graziano Grugni, Antonino Crinò, Assumpta Caixàs, Christine Poitou, Raquel Corripio, Rosa M Nieuwenhuize, Aart J van der Lely, Laura C G de Graaff

Vol.108 Issue 11

原発性副甲状腺機能亢進症手術後の長期再発率

Long-term Recurrence Rates After Surgery in Primary Hyperparathyroidism

Muizz Zaman, Laxshika Raveendran, Ayla Senay, Harlan Sayles, Runa Acharya, Mashaal Dhir
 

Vol.108 Issue 11

先天性副腎過形成(CAH)患者において新生児スクリーニングが成人身長に及ぼす影響

Impact of Newborn Screening on Adult Height in Patients With Congenital Adrenal Hyperplasia (CAH)

Heike Hoyer-Kuhn, Alexander J Eckert, Gerhard Binder, Walter Bonfig, Angelika Dübbers, Stefan Riedl, Joachim Woelfle, Helmuth G Dörr, Reinhard W Holl

Vol.108 Issue 11

保存期慢性腎臓病患者の二次性副甲状腺機能亢進症に対する治療法としてのパリカルシトール及びcalcifediol徐放製剤:ネットワークメタアナリシスの結果

Paricalcitol and Extended-Release Calcifediol for Treatment of Secondary Hyperparathyroidism in Non-Dialysis Chronic Kidney Disease: Results From a Network Meta-Analysis

Matteo Franchi, Joel Gunnarsson, Emilio Gonzales-Parra, Anibal Ferreira, Oskar Ström, Giovanni Corrao

Vol.108 Issue 11

副腎不全の早期発見:副腎皮質ジストロフィーの新生児スクリーニングがもたらす効果

Early Detection of Adrenal Insufficiency: The Impact of Newborn Screening for Adrenoleukodystrophy

Jonanlis Ramirez Alcantara, Natalie R Grant, Swathi Sethuram, Amanda Nagy, Catherine Becker, Inderneel Sahai, Takara Stanley, Alyssa Halper, Florian S Eichler

Vol.108 Issue 11

肥満及び非肥満妊娠糖尿病患者における代謝プロファイル

Metabolomic Profiles of Nonobese and Obese Women With Gestational Diabetes

Heidi Sormunen-Harju, Emilia Huvinen, Polina V Girchenko, Eero Kajantie, Pia M Villa, Esa K Hämäläinen, Marius Lahti-Pulkkinen, Hannele Laivuori, Katri Räikkönen, Saila B Koivusalo

Vol.108 Issue 11

CRF1受容体拮抗薬crinecerfontは思春期の先天性副腎過形成患者において副腎アンドロゲン値を低下させる

Crinecerfont, a CRF1 Receptor Antagonist, Lowers Adrenal Androgens in Adolescents With Congenital Adrenal Hyperplasia

Ron S Newfield, Kyriakie Sarafoglou, Patricia Y Fechner, Natalie J Nokoff, Richard J Auchus, Maria G Vogiatzi, George S Jeha, Nagdeep Giri, Eiry Roberts, Julia Sturgeon, Jean L Chan, Robert H Farber

Vol.108 Issue 11

骨折の生涯リスクの遺伝的予測

Genetic Prediction of Lifetime Risk of Fracture

Thao P Ho-Le, Thach S Tran, Huy G Nguyen, Jacqueline R Center, John A Eisman, Tuan V Nguyen

Vol.108 Issue 11

糖尿病患者におけるカナグリフロジンと代謝異常関連脂肪性肝疾患:CANVAS試験からの新たな知見

Canagliflozin and Metabolic Associated Fatty Liver Disease in Patients With Diabetes Mellitus: New Insights From CANVAS

Angel N Borisov, Alexander Kutz, Emanuel R Christ, Markus H Heim, Fahim Ebrahimi

Vol.108 Issue 11

小児X染色体連鎖性低リン血症におけるブロスマブとリン酸塩/活性型ビタミンDとの比較:用量レベル別のサブグループ解析

Burosumab vs Phosphate/Active Vitamin D in Pediatric X-Linked Hypophosphatemia: A Subgroup Analysis by Dose Level

Erik A Imel, Francis H Glorieux, Michael P Whyte, Anthony A Portale, Craig F Munns, Ola Nilsson, Jill H Simmons, Raja Padidela, Noriyuki Namba, Hae Il Cheong, Pisit Pitukcheewanont, Etienne Sochett, Wolfgang Högler, Koji Muroya, Hiroyuki Tanaka, Gary S Gottesman, Andrew Biggin, Farzana Perwad, Angel Chen, Mary Scott Roberts, Leanne M Ward

Vol.108 Issue 11

ベセスダ分類IIIまたはVIの甲状腺結節50,734例を対象としたThyroSeq v3による分子プロファイリング:個別化医療に向けての意義

Molecular Profiling of 50 734 Bethesda III-VI Thyroid Nodules by ThyroSeq v3: Implications for Personalized Management

Simion Chiosea, Steven P Hodak, Linwah Yip, Devaprabu Abraham, Chelsey Baldwin, Zubair Baloch, Seza A Gulec, Zeina C Hannoush, Bryan R Haugen, Lija Joseph, Atil Y Kargi, Elham Khanafshar, Masha J Livhits, Bryan McIver, Kepal Patel, Snehal G Patel, Gregory W Randolph, Ashok R Shaha, Jyotirmay Sharma, Nikolaos Stathatos, Annemieke van Zante, Sally E Carty, Yuri E Nikiforov, Marina N Nikiforova